Abstract: Lymphangiodysplasia is a common vascular disease in children. This paper summarizes the imaging characteristics, anatomical basis and pathophysiological mechanism of lymphatic reflux disorder, lymphangiodilation, lymphangiopathy and lymphangiomatosis through different imaging techniques and methods, so as to intuitively display the characteristic imaging changes of lymphatic dysplasia. It provides accurate and appropriate diagnosis and treatment information, as well as the means of monitoring curative effect for clinical diagnosis and treatment of lymphatic diseases.